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POEMS综合征29例临床分析
引用本文:张晓飞,张映琦,陈康宁,史树贵,范文辉,胡俊. POEMS综合征29例临床分析[J]. 疑难病杂志, 2011, 10(7): 492-494. DOI: 10.3969/j.issn.1671-6450.2011.07.005
作者姓名:张晓飞  张映琦  陈康宁  史树贵  范文辉  胡俊
作者单位:1. 西南医院神经内科
2. 第三军医大学附属西南医院神经内科,重庆市,400038
摘    要:目的分析POEMS综合征的临床特征,加深对POEMS综合征的认识。方法回顾性分析近6年来确诊的29例POEMS综合征的临床特点,结合相关文献进行分析。结果所有病例均有周围神经病变,多伴有肝、脾和(或)淋巴结肿大、多种内分泌病变、皮肤改变、水肿及骨髓浆细胞增多。结论 POEMS综合征是一少见的多系统损害疾病,临床表现复杂多样,诊断较难。对不明原因周围神经损害的患者,特别是合并皮肤改变、肢端水肿或者内分泌及代谢异常症状时要想到该病的可能。

关 键 词:POEMS综合征  多发性周围神经病  M蛋白  脏器肿大  内分泌疾病

POEMS syndrome:A clinical analysis of 29 cases
ZHANG Xiao-fei,ZHANG Ying-qi,CHEN Kang-ning,et al.. POEMS syndrome:A clinical analysis of 29 cases[J]. Journal of Difficult and Complicated Cases, 2011, 10(7): 492-494. DOI: 10.3969/j.issn.1671-6450.2011.07.005
Authors:ZHANG Xiao-fei  ZHANG Ying-qi  CHEN Kang-ning  et al.
Affiliation:ZHANG Xiao-fei~*,ZHANG Ying-qi,CHEN Kang-ning,et al.* Department of Geriatrics,107th Hospital of PLA,Shandong Province,Yantai 264000,China
Abstract:Objective To analyze the clinical characteristics of POEMS syndrome for improving clinical understanding of this syndrome.Methods 29 cases of POEMS syndrome were reviewed retrospectively which were diagnosed in last 6 years and analyzed with the pertinent literatures.Results All patients were shown to have peripheral neuropathy,hepatomegaly, splenomegaly,lymphadenectasis,endocrinopathy,skin changes,edema and plastcytosis in bone marrow were commonly found in these patients.Conclusion It's a rare multisystem...
Keywords:POEMS syndrome  Multiple peripheral neuropathy  M protein  Organomegaly  Endocrinopathy  
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