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Kartagener综合征的影像学诊断
引用本文:刘进康,夏宇,王维,张子署.Kartagener综合征的影像学诊断[J].临床放射学杂志,2005,24(5):403-405.
作者姓名:刘进康  夏宇  王维  张子署
作者单位:410008,长沙,中南大学湘雅医院放射;410009,长沙,中南大学湘雅三医院放射;410011,长沙,中南大学湘雅二医院放射
摘    要:目的探讨Kanagener综合征的影像学表现及其诊断价值。资料与方法回顾性分析12例Kanagener综合征的影像学表现,12例均摄有胸部及副鼻窦x线片,其中9例行CT检查,6例行HRCT扫描。结果所有病例均表现有右位心;5例胸片可诊断支气管扩张症,CT及HRCT示支气管扩张症表现为“印戒征”、“蜂窝征”、“轨道征”、“胸膜下征”;12例均有副鼻窦炎表现。结论影像学表现是临床诊断Kanagener综合征的主要依据。

关 键 词:Kartagener综合征  罕见病  影像诊断

Imaging Diagnosis of Kartagener Syndrome
LIU Jinkang,XIA Yu,WANG Wei,et al..Imaging Diagnosis of Kartagener Syndrome[J].Journal of Clinical Radiology,2005,24(5):403-405.
Authors:LIU Jinkang  XIA Yu  WANG Wei  
Institution:LIU Jinkang,XIA Yu,WANG Wei,et al. Department of Radiology,The Affiliated Xiangya Hospital,Centralsouth University,Changsha,Hunan Province 410008,P. R. China
Abstract:Objective To evaluate imaging diagnosis of Kartagener syndrome. Materials and Methods Both chest film and paranasal sinus film of 12 cases with Kartagener syndrome were analyzed retrospectively. Of 12 cases, CT were performed in 9 cases and HRCT in 6 cases.Results All cases were presented dexiocardia and chronic paranasal sinusitis. Bronchiectasis was seen in chest films of 5 cases. The HRCT findings of bronchietasis included ring, beehive, track sign. Conclusion Imaging findings plays an important role in the diagnosis of Kartagener syndrome.
Keywords:Kartagener syndrome  Infrequent disease  Imaging diagnosis
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