特发性腹膜后纤维化误诊一例并文献复习

目的提高对特发性腹膜后纤维化的认识，避免或减少对该病的误诊。方法报告我院1例特发性腹膜后纤维化的临床表现，辅助检查和治疗情况，并结合文献资料进行复习。结果人院后给以彩色多普勒超声、MR、ECT、血管造影等辅助检查明确诊断后，行左肾动脉放置支架和血液透析，同时联合免疫抑制治疗，近期临床治疗效果满意。结论IRPF临床表现缺乏特异性．影像学检查是明确诊断的重要举措。解除梗阻后继续给以免疫抑制治疗，对获得远期治疗效果有重要意义，但仍需要大宗资料进行临床论证。

Misdiagnosis of 1 case with Idiopathic retroperitoneal fibrosis and literature review

Objective To improve the recognition of idiopathic retroperitoneal fibrosis （IRPF） for avoiding or reducing the misdiagnosis. Methods A case of IRPF on the clinical manifestation, assisted examination and treatment was reported and literature data were reviewed. Results 1 case of IRPF was confirmed by Colour Doppler Ultrasonography, MRA and ECT as well as angiography after hospitalization. The Short-term therapeutic efficacy was satisfactory after treatment with left renal artery stent placement and hemodialysis combined with immunosuppressive drugs simultaneously. Conclusion Clinical manifestation of IRPF is lack of specificity. Imaging examination is very important to confirm diggnosis. A better prognosis depends on sequential therapy with immunosuppressive agents after relief of stricture of renal artery or obstruction of ureter, but this viewpoint still needs support from clinical analysis of a large amount of data.