| Abstract: | Incontinentia pigmenti is a rare X-linked genodermatosis that affects mainlyfemale neonates. The first manifestation occurs in the early neonatal period andprogresses through four stages: vesicular, verruciform, hyperpigmented andhypopigmented. Clinical features also manifest themselves through changes in theteeth, eyes, hair, central nervous system, bone structures, skeletal musculatureand immune system. The authors report the case of a patient with cutaneouslesions and histological findings that are compatible with the vesicular stage,emphasizing the importance of early diagnosis and appropriate therapeuticmanagement. |
