(1) Division of Paediatric Surgery, Johannesburg Hospital, University of the Witwatersrand, Johannesburg, South Africa;(2) P.O. Box 413213, 2024 Craighall, Johannesburg, Republic of South Africa
Abstract:
Appendico-cutaneous fistulae are rare. We describe a 12-year-old girl with cystic fibrosis (CF) and a chronically draining sinus in the right iliac fossa, found to be a primary appendico-cutaneous fistula. Misdiagnosis of right iliac fossa pain in patients with CF and the preponderance of complicated disease frequently lead to manifestations of appendicitis rarely seen in usual clinical practice.