| Abstract: | A 52-year-old man had an atypical cutaneous hemangioma on the right side of his neck. He had suffered from hypertension since he was 20 years old with marked differences in blood pressure in each arm. He had no other clinical symptoms. Angiography revealed that the patient had a typical aortitis syndrome which included obstruction of the left common carotid artery, stenosis of the left subclavicular artery, stenosis of both renal arteries and an irregular shadow of the abdominal aorta. On the area of the skin lesion there were a slightly dilated feeding artery and an obscure net work of arteries. No sign of direct A-V shunt was seen. This hemangioma could be pure capillary malformation in the angiographic classification by Merland et al. Renin activity and angiotensin I were high. Histopathological examination of the skin lesion revealed dilatation and enlargement of small veins in the upper dermis and increased arteries and veins of medium size from the deep dermis to subcutaneous fat tissue. This atypical cutaneous hemangioma is thought to be an important skin marker for this syndrome. |
