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MR imaging appearance of laryngeal atresia (congenital high airway obstruction syndrome): unique course in a fetus
Authors:Shigeko Kuwashima  Kazuhiro Kitajima  Yasushi Kaji  Hiroshi Watanabe  Yoshiyuki Watabe  Hiroshi Suzumura
Affiliation:(1) Department of Radiology, Dokkyo Medical University, 880 Kitakobayashi, Mibu, Shimotsuga-gun Tochigi, 321-0273, Japan;(2) Department of Obstetrics and Gynecology, Dokkyo Medical University, Mibu, Japan;(3) Department of Pediatrics, Dokkyo Medical University, Mibu, Japan
Abstract:Congenital high airway obstruction syndrome (CHAOS) is a rare life-threatening syndrome. Most cases are diagnosed prenatally by US. We report a fetus with this syndrome that showed a unique course revealed on MRI. Ultrasonography at 22 weeks demonstrated that the fetus had ascites and bilaterally enlarged hyperechoic lungs. Congenital infection, congenital cystic adenomatoid malformation or CHAOS was suspected. Subsequent MRI performed at 24 weeks demonstrated bilaterally enlarged high-signal lungs, dilated bronchi, massive ascites, subcutaneous oedema and polyhydramnios. MRI confirmed the diagnosis of CHAOS. A second MRI at 35 weeks showed that the bilateral lung enlargement, ascites, oedema and polyhydramnios had resolved, but that the appearance of the airway was unchanged. The infant was delivered by caesarean section at 38 weeks of gestation and immediate tracheostomy was performed. This spontaneous regression was explained by a tracheo-oesophageal fistula that may have decreased the intrathoracic pressure.
Keywords:Fetus  Congenital high airway obstruction  MRI
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