快速消退型先天性血管瘤的临床表现和影像学特征

目的 研究一种特殊的婴幼儿血管肿瘤的临床表现和影像学特征.方法 2006年7月到2008年5月回顾了11例被诊断为快速消退型先天性血管瘤患儿的临床资料.影像学资料包括5例患儿的MRI和4例患儿的计算机体层摄影血管造影术.结果 本组所有的快速消退型先天性血管瘤患儿肿物均未治疗而在1岁前消退.病灶外观主要表现为三种类型:肿物呈紫色隆起,伴有肿物邻近部位静脉扩张(n=4);肿物颜色浅灰色,伴有肿物表面皮肤毛细血管扩张和肿物周缘发白晕圈(n=3);肿物紫色平坦,质地较硬(n=3).仅1例病灶质地柔软,肿物位置较深,表面皮肤颜色正常.肿物平均直径5.6cm.MRI和CTA表现和普通婴幼儿血管瘤相似,部分病灶在MRI上表现为均质性较差和更大的流空信号.结论 快速消退型先天性血管瘤是一种出生时即已增生完全的特殊的先天性血管肿瘤,出生后消退迅速,根据病史和临床表现容易诊断,不推荐激进的治疗.

Study of clinical and radiological features of rapidly involuting congenital hemangioma

Objective To study the clinical and radiological features of infantile congenital he-mangioma. Methods From June, 2006 to May. 2008, the clinical and imaging findings of 11 infants with rapidly involuting congenital hemangiorna (RICH) were analyzed restropectively. Diagnosis was made by clinical and radiologic examinations or biopsy. Results All these infants with RICH regressed before the age of 12 months without any therapy. The main morphologic forms of RICH were classified into 3 categories: (1) light purple staining with local variocose (n=4); (2) lesions in light gray color with capillary telangiectasias and white halation (n=3); and (3)purple in color, rather hard and flatten (n=3). The mean diameter of lesion was 5.6 cm The demonstration of RICH on MRI and CTA were very similar to those of common infantile hemangioma, with some RICH having areas of inhomogenei-ty and larger flow voids on MRI. Conclusions RICH is vascular lesions that grow rapidly during the first few months of life and then begin to involute rapidly, therefore no therapy is necessary.