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Intravenous γ-Globulin Therapy in Diamond-Blackfan Anemia |
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| Authors: | Shin-ichi Sumimoto MD Masahiko Kawai MD Yoshiki Kasajima MD Torata Hamamoto MD |
| Institution: | Department of Pediatrics, Sumitomo Hospital, Osaka |
| Abstract: | Pure red cell aplasia (PRCA) is a rare disorder of erythrocyte production which is believed to have an autoimmune basis in most cases. Diamond-Blackfan anemia (DBA) is one type of congenital PRCA. Since PRCA has been reported to respond to intravenous γ-globulin (IVGG) therapy, we administered IVGG to a 2 year old girl with DBA resistant to corticosteroids and observed slight therapeutic effect. |
| Keywords: | Diamond-Blackfan anemia (DBA) Intravenous γ-globulin (IVGG) therapy Pure red cell aplasia (PRCA) |