Imperforate anus with congenital short colon (pouch colon syndrome)

There have not been many case reports of imperforate anus with congenital short colon (pouch colon syndrome). On the Indian subcontinent it is a commonly encountered entity in high ano rectal anomalies. Eighteen cases of pouch colon syndrome were treated in a period of 2 1/2 years, which constituted 26.08% of all high anorectal anomalies. All patients were male and the invertogram was diagnostic in all cases. Associated congenital malformations were common. Most of the patients were in poor general condition at the time of admission. Post-operative pulmonary complications and septicaemia were common. Pouch colostomy was performed in all cases. In the immediate post-operative period 44.44% of all patients died. A pull-through colonorraphy was done as a definitive procedure in 1 case.