致心律失常性右心室心肌病临床分析

目的 :分析致心律失常性右心室心肌病的临床特点。方法 :将 2 3例致心律失常性右心室心肌病患者常规行超声心动图、心电图、胸片、动态心电图、心房调搏及心内电生理检查。结果 :本组 2 3例患者多有晕厥发作 ,频发室性早搏 (95 7% ) ,右心室源性短阵室速 (87% ) ,心电图多为右束支传导阻滞 (87% ) ,超声心动图右心室内径为 (5 0 1± 8 83)mm ,右心房内径为 (48± 8 79)mm ,右心室与左心室舒张末期内径之比为 1 0 9,右心功能减退 ,射血分数 (EF)为(0 32 5± 0 0 90 2 )。结论 :致心律失常性右心室心肌病 ,多有发作性晕厥 ,右束支传导阻滞 ,频发室早及左束支传导阻滞型室速 ,右心室、右心房增大 ,右心室功能减退 ,右心室与左心室舒张末期内径之比增大

Clinical analysis of arrthythmogenic right ventricular cardiomyopathy

Objective To investigate the clinical features of arrthythmogenic right ventricular cardiomyopathy (ARVC), and to evaluate the diagnosis of ARVC. Methods Twenty three cases of ARVC underwent ECG, chest x ray, Holter, transesophageal atrial pacing (TEAP) and intracardiac electrophysiological examination. Results A syncope attack occurred; the percentage of frequent ventricular premature beats was 95.7%, salvos of the right ventricular originated ventricular tachycardia (VT) was 87%, and the right bundle branch block (RBBB) demonstrated by ECG was 87%; UCG showed that the enlarged right ventricular diametric was (50.1±8.83)mm, and the right atrium diametric was (48±8.79)mm; the ratio of right ventricular diametric to left ventricular diametric in the end diastolic period was 1.09. The right ventricular function ejection fraction: (0.325±0.0902)] decreased, which was confirmed by echocardiogram. Conclusion The diagnosis of ARVE can be established on the basis of the repeated syncope attack; RBBB, frequent ventricular premature beats, VT of LBBB patterms, an enlarged right heart and decreased right ventricular function can be found; the ratio of right ventricular dimaetric to left ventricular diametric increases in the end diastolic period.