The term “myopathic pattern” is applied to the electrocardiographic finding of R/S in lead V1 of more than 1.5 in association with deep Q and prominent R waves in leads V4-V6.1 Such findings are characteristic of Duchenne's pseudohypertrophic muscular dystrophy and reportedly do not occur in other types of muscular dystrophy or myopathy.2,3The purpose of this paper is to describe a case of myotonia dystrophica with the Duchenne electrocardiographic pattern.