双肾血管平滑肌脂肪瘤伴发结节性硬化症的诊治

目的 探讨双肾血管平滑肌脂肪瘤(AML)伴结节性硬化症(TSC)的临床特点,以提高该病的诊治水平.方法 报告本院收治1例双肾AML伴TSC的临床诊治资料并复习文献.结果经过B超、CT及MRI检查确诊.本例女性患者双肾CT及MRI检查发现肿瘤内特异性脂肪密度组织,头颅CT检查发现典型的大脑钙化结节灶.因患者全身多发占位,...

Diagnosis and treatment of bilateral multiple renal angiomyolipomas associated with tuberous sclerosis

Objectives To study the clinical features of renal angiomyolipomas with tuberous sclerosis and to improve the diagnosis and treatment. Methods The diagnosis and treatment of 1 case of bilateral multiple renal angiomyolipomas associated with tuberous scleros were reported and review the articles. Results The diagnosis of renal angiomyolipomas associated with tuberous sclerosisi was confirmed by ultrasonography and CT and MRI scan ning. However. the giant renal angiomyolipomas can be diagnosed from renal CT and MRI scan which demonstrate characteristic fatty tissue. Brain CT revealed classical calcified cortical tuber and subependymal nodule. Regular mo nitoring of the patient with conservative therapy was adopted for occupying multiple body and surgical treatment re sults were poor. Conclusions Ultrasonography and CT and MRI are important methods to diagnose and the choice of treatment is based on tumor size,distribution pattern,symptoms and associated progression.