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儿童心肌病诊断治疗10年回顾
引用本文:章旭,黄美蓉,陈树宝,武育蓉,柏屏,郭颖,傅立军,赵鹏军,高伟,李奋,李筠,张玉奇.儿童心肌病诊断治疗10年回顾[J].临床儿科杂志,2011,29(4).
作者姓名:章旭  黄美蓉  陈树宝  武育蓉  柏屏  郭颖  傅立军  赵鹏军  高伟  李奋  李筠  张玉奇
作者单位:上海交通大学医学院附属上海儿童医学中心心内科,上海,200127
摘    要:目的 了解小儿心肌病的流行病学特征、临床特点、治疗及预后.方法 对1999年1月 - 2009年12月在上海儿童医学中心心内科诊治的心肌病病例及随访资料进行整理分析.结果 共收集病例339例,男204例,女135例;平均年龄45.26个月(1 d ~ 15岁).失访82例,死亡96例.扩张型心肌病(DCM)187例(55.2%),失访42例(22.5%),死亡67例(35.8%);肥厚型心肌病(HCM)80例(23.6%),失访23例,死亡11例;限制型心肌病(RCM)16例(4.7%);未分类型心肌病(UCM)55例(16.2%);致心律失常型右室型心肌病(ARVC)1例(0.3%).DCM平均左心室射血分数(LVEF)(32.9 ± 0.69)%,HCM平均LVEF(79.04 ± 2.70)%.HCM中梗阻型39例,死亡2例(5.1%);非梗阻型41例,死亡9例(22.0%)(P = 0.02).RCM平均LVEF(63.7 ± 2.3%),死亡5例(31.3%).UCM主要是心肌致密化不全病例,平均LVEF(44.88 ± 1.97)%,死亡12例(21.8%).ARVC仅1例,失访.结论 儿童心肌病中DCM最常见.HCM梗阻型与非梗阻型发病率相近,后者病死率明显高于前者.

关 键 词:心肌病  流行病学  临床特点  儿童

Retrospective analysis of the diagnosis and treatment of pediatric cardiomyopathy in last ten years
ZHANG Xu,HUANG Mei-rong,CHEN Shu-bao,WU Yu-rong,BAI Ping,GUO Ying,FU Li-jun,ZHAO Peng-jun,GAO Wei,LI Fen,LI Yun,ZHANG Yu-qi.Retrospective analysis of the diagnosis and treatment of pediatric cardiomyopathy in last ten years[J].The Journal of Clinical Pediatrics,2011,29(4).
Authors:ZHANG Xu  HUANG Mei-rong  CHEN Shu-bao  WU Yu-rong  BAI Ping  GUO Ying  FU Li-jun  ZHAO Peng-jun  GAO Wei  LI Fen  LI Yun  ZHANG Yu-qi
Institution:ZHANG Xu,HUANG Mei-rong,CHEN Shu-bao,WU Yu-rong,BAI Ping,GUO Ying,FU Li-jun,ZHAO Peng-jun,GAO Wei,LI Fen,LI Yun,ZHANG Yu-qi(Department of Pediatric Cardiology,Shanghai Children's Medical Center,Shanghai Jiaotong University School of Medicine,Shanghai 200127,China)
Abstract:Objective To explore the epidemiological characteristics,clinical features,treatment and prognosis profile of pediatric cardiomyopathy.Methods Retrospective analysis was done on the clinical data of patients diagnosed with cardiomyopathies from Jan 1999 to Dec 2009 in Shanghai Children's Medical Center.Results The data on a total of 339 patients(204 males and 135 females)diagnosed with cardiomyopathy were collected.The mean age was 46.26 months(1d to 15 years).Eighty-two patients were lost to follow up.Nine...
Keywords:cardiomyopathy  epidemiology  clinical feature  children  
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