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黏液炎性纤维母细胞肉瘤与结节性腱鞘炎的相关意义
引用本文:螘国铮,陈柯,窦红漫,丁敏,翁海燕,胡闻,王晓秋. 黏液炎性纤维母细胞肉瘤与结节性腱鞘炎的相关意义[J]. 临床与实验病理学杂志, 2008, 24(3)
作者姓名:螘国铮  陈柯  窦红漫  丁敏  翁海燕  胡闻  王晓秋
作者单位:安徽省立医院病理科,合肥,230001;安徽中医学院附院病理科,合肥,230031
摘    要:目的 探讨黏液炎性纤维母细胞肉瘤与结节性腱鞘炎的相关意义.方法 对1例复发于结节性腱鞘炎的黏液炎性纤维母细胞肉瘤进行光镜和免疫组织化学检查.结果 证实黏液炎性纤维母细胞肉瘤具有特征性异型细胞,包括假脂肪母细胞、印戒样细胞及相似于病毒细胞、神经节细胞和R-S细胞.组织结构由明显黏液样区、纤维透明变性和炎症性病变混杂组成.肿瘤细胞表达vimentin弥漫阳性,CD34和CD68部分阳性,大多数淋巴细胞表达CD3和CD45RO阳性.结节性腱鞘炎不出现特征性异型细胞和明显黏液样区.结论黏液炎性纤维母细胞肉瘤是一种低度恶性肿瘤,好发于肢端,生长缓慢,复发率高,与肢端结节性腱鞘炎的临床病理和免疫表型有明显相似处,惟没有特征性异型细胞和明显黏液,MIFS和结节性腱鞘炎相互关系有待进一步研究.

关 键 词:纤维母细胞肉瘤  结节性腱鞘炎  临床病理  免疫组织化学

Significance of relationship between myxoinflammatory fibroblastic sarcoma and nodular tendosynovitis
YI Guo-zheng,CHEN Ke,DOU Hong-man,DING Ming,WENG Hai-yan,HU Wen,WANG Xiao-qiu. Significance of relationship between myxoinflammatory fibroblastic sarcoma and nodular tendosynovitis[J]. Chinese Journal of Clinical and Experimental Pathology, 2008, 24(3)
Authors:YI Guo-zheng  CHEN Ke  DOU Hong-man  DING Ming  WENG Hai-yan  HU Wen  WANG Xiao-qiu
Affiliation:1Department Pathology;Anhui Provincial Hospital;Hefei 230001;China;2Department Pathology;Anhui College of Traditional Chinese Medicine;Hefei 230031;China
Abstract:Purpose To investigate the significance of the relationship between myxoinflammatory fibroblastic sarcoma(MIFS) and nodular tendosynovitis.Methods One case of MIFS arising from nodular tendosynovitis was studied by light microscopy,and immunohistochemistry.Results MIFS showed distinctive atypical cells,including pseudolipoblasts,signet-ring like cells and resembling virocytes,ganglion cells or R-S like cells.The architecture of MIFS was characterized by the mixture of prominent myxoid areas,fibrous hyaline ...
Keywords:fibroblastic sarcoma  nodular tendosynovitis  clinical pathology  immunohistochemistry  
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