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Cutaneous manifestation of IgG4-related disease mimicking dermatitis artefacta
Authors:Vivek Ashoka Menon  Elissa Tong  Dana Rose-Marie Louise Slape  Tai Anh Phan  Renee CF Chan
Affiliation:1. Anatomical Pathology Department, NSW Health Pathology, Concord Repatriation General Hospital, Concord, New South Wales, Australia;2. Dermatology Department, NSW Health, Concord Repatriation General Hospital, Concord, New South Wales, Australia
Abstract:Dermatitis artefacta is a self-inflicted cutaneous disease presenting as sharply delineated ulcers, usually in accessible sites such as the head and neck. IgG4-related disease (IgG4-RD) is a recently recognised immune-mediated condition causing a fibroinflammatory process, resulting in the formation of tumefactive lesions in various organs, rarely presenting primarily in the skin. We report a case of cutaneous IgG4-RD clinically presenting as dermatitis artefacta.
Keywords:cutaneous IgG4-RD  dermatitis artefacta  IgG4  IgG4-related disease
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