Lowe's syndrome with Fanconi syndrome for ocular surgery: perioperative anesthetic considerations |
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Authors: | Pandey Ravindra Garg Rakesh Chakravarty Chandrashish Darlong Vanlal Punj Jyotsna Chandralekha |
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Institution: | a Department of Anaesthesiology and Intensive Care, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110029, India |
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Abstract: | Lowe's syndrome is a rare inherited metabolic disorder characterized by mental retardation, kidney malfunction, and abnormalities of the eyes and bones. A 4 month-old child with Lowe's and Fanconi's syndrome, undergoing bilateral congenital cataract surgery, is presented. Preoperative electrolyte imbalance was corrected by potassium, calcium, magnesium, phosphate, and bicarbonate supplementation. Anesthesia was administered uneventfully using appropriate anesthetic agents and monitoring. Adequate preoperative evaluation and optimization, along with selection of anesthetic agents and fluid and electrolyte management with appropriate perioperative monitoring, is key to a successful outcome. |
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Keywords: | Anesthesia Fanconi syndrome Lowe's syndrome Oculocerebrorenal syndrome of Lowe |
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