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良性对称性脂肪瘤病的诊断和治疗(附6例报告)
引用本文:阚英南,姚平,辛伟红,陈倩倩,王骏,岳健,朱嘉靖.良性对称性脂肪瘤病的诊断和治疗(附6例报告)[J].临床耳鼻咽喉头颈外科杂志,2010,24(3).
作者姓名:阚英南  姚平  辛伟红  陈倩倩  王骏  岳健  朱嘉靖
作者单位:吉林大学中日联谊医院耳鼻咽喉头颈外科,长春,130031
摘    要:目的:探讨良性对称性脂肪瘤病(BSL)的诊断和治疗。方法:结合我院收治的6例BSL患者,回顾性分析BSL的临床症状、体征、诊断及治疗,并结合文献进行探讨。结果:6例均以颈项部大量皮下脂肪堆积为主要表现,其中1例伴有双侧上臂近肘窝处皮下脂肪堆积呈对称性隆起。6例患者伴左心舒张功能改变、糖耐量减低、阻塞性睡眠呼吸暂停低通气综合征、Ⅱ型糖尿病及高尿酸血症中的1项或多项,其中1例患者同时出现上述症状,除1例女性患者未见肝功能改变外其余5例男性患者均出现。5例男性患者均有长期酗酒史。除1例拒绝治疗外,其余5例行彻底切除术及戒酒,术后随访3个月~4年,1例术后3年后复发,未行再次治疗,其余4例无复发。所有患者术后病理诊断为无包膜脂肪组织。结论:BSL是一种脂肪代谢障碍引起的脂肪组织弥漫性、对称性沉积于颈肩部皮下浅筋膜间隙和(或)深筋膜间隙的良性疾病。患者以中年男性居多,长期的酗酒史及典型的临床表现对于该病的诊断有一定帮助,对于影响美观及功能的患者手术疗效较理想。

关 键 词:脂肪瘤病  诊断  治疗  

Recent progress on diagnosis and treatment of benign symmetric lipomatosis
KAN Yingnan,YAO Ping,XIN Weihong,CHEN Qianqian,WANG Jun,YUE Jian,ZHU Jiajing.Recent progress on diagnosis and treatment of benign symmetric lipomatosis[J].Journal of Clinical Otorhinolaryngology,2010,24(3).
Authors:KAN Yingnan  YAO Ping  XIN Weihong  CHEN Qianqian  WANG Jun  YUE Jian  ZHU Jiajing
Institution:Department of Otolaryngology Head and Neck Surgery/a>;China-Japan Union Hospital of Jilin University/a>;Changchun/a>;130031/a>;China
Abstract:Objective:To introduce recent progress on diagnosis and treatment of benign symmetric lipomatosis(BSL).Method:Detailed clinical data of 6 patients with BSL were reviewed and analyzed.We present a summary of the clinical symptoms,physical sign,diagnosis and therapeutic methods of BSL. And related literatures were discussed together.Result:All of 6 patients have excessive subcutaneous fat deposit predominantly around neck.One patients had upper extremity localizations. Six patients had the complication of lef...
Keywords:lipomatosis  diagnosis  treatment  
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