Extra nodal Rosai Dorfman disease masquerading as metastatic soft tissue sarcoma- A case report |
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| Affiliation: | 1. Department of Orthopaedic Surgery, Cairo University Faculty of Medicine, Cairo, Egypt;2. Department of Orthopaedic Surgery, Menoufia University Faculty of Medicine, Shebin El-Kom, Menoufia, Egypt;1. Diploma in Gait Analysis (Stratchclyde), Consultant Adult and Paediatric Orthopaedic Surgeon, King''s College Hospital, London, SE5 9RS, United Kingdom;2. Sports/Exercise Medicine, Specialist Registrar in Orthopaedics, King''s College Hospital, London, SE5 9RS, United Kingdom;1. Institute of Advanced Orthopaedics, MOSC Medical College, Kolenchery, 682311, Ernakulam, Kerala, India;2. Department of Radio Diagnosis, MOSC Medical College, Kolenchery, 682311, Ernakulam, Kerala, India;1. Departments of Musculoskeletal Radiology, Royal Orthopaedic Hospital, Birmingham, UK;2. Departments of Spinal Surgery, Royal Orthopaedic Hospital, Birmingham, UK;3. Departments of Musculoskeletal Radiology, Royal National Orthopaedic Hospital, Stanmore, London, UK;1. Orthopaedic and Trauma Surgery Department, University of Pisa, Via Paradisa 2, 56100, Pisa, PI, Italy;2. Radiology Department, University of Pisa, Via Paradisa 2, 56100, Pisa, PI, Italy;3. Neuroradiology Department, University of Pisa, Via Paradisa 2, 56100, Pisa, PI, Italy |
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| Abstract: | Rosai Dorfman disease is rare benign disease of phagocytic histiocytosis usually present as painless massive lymphadenopathy. Extra nodal presentation of Rosai Dorfman disease is rare but also described. We hereby describe an unusual presentation of the extra nodal Rosai Dorfman disease with rapidly growing soft tissue lesion in the left thigh with associated osseous lesions in the right distal femur, left distal femur, left proximal tibia and presence of solitary pulmonary nodule. This case is unique as clinical presentation highly suspicious of soft tissue sarcoma but excision biopsy of thigh lesion showed Rosai Dorfman disease.Though RDD in extremities has been described in limited number of cases, to the best of our knowledge this is first case of lower extremity RDD associated with osseous lesions and pulmonary nodule but without lymphadenopathy. |
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| Keywords: | Rosai-dorfman disease Soft tissue sarcoma Metastasis Differential diagnosis |
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