6例经典型枫糖尿病患儿行肝移植的术后护理

总结6例经典型枫糖尿病患儿行肝移植的术后护理经验。护理要点包括：精确服用免疫抑制剂,预防急性排异反应;早期康复功能锻炼,促进神经系统发育;密切观察病情变化,做好消化道出血的急救护理;实施结构化皮肤护理,减轻尿布性皮炎症状;提供多形式支持,缓解家属压力;实施互联网+随访模式,持续家庭康复护理。经过精心的治疗与护理,6例患儿术后康复出院,随访15 d~4个月,恢复效果良好。

Postoperative nursing care of 6 children with classic maple syrup urine disease undergoing liver transplantation

This article summarized the postoperative nursing experience of 6 children with classic maple syrup urine disease undergoing liver transplantation. Key points of nursing care included：precisely take immunosuppressants to prevent acute rejection;early rehabilitation exercises to promote the development of the nervous system;closely observe changes in the condition and do emergency care for gastrointestinal bleeding;structured skin care to reduce diaper dermatitis;provide multiple forms of support to relieve family pressure;implementation of the Internet + follow-up model,continuous family rehabilitation care. After careful treatment and care,the 6 children recovered and were discharged after surgery. They were followed up for 15 days to 4 months and recovered well up to now.