原发性胸膜脂肪肉瘤的临床特点

目的原发性胸膜脂肪肉瘤是一种非常罕见的肿瘤，本文报道国内首例病例，并探讨其临床特点、诊断及治疗。方法分析我院近期发现的1例原发性胸膜脂肪肉瘤的临床资料并复习相关文献。结果原发性胸膜脂肪肉瘤全世界仅报道17例（包括此例）。本病好发于男性，中老年人多见，病理类型以黏液型多见；临床症状以胸痛和气促最常见；诊断主要依靠影像学和开胸探查。目前治疗推荐手术切除加辅助放疗。结论原发性胸膜脂肪肉瘤的治疗和预后的评估有待进一步积累资料。

Liposarcoma of the pleura: clinical characteristics

Objective Primary liposarcoma of the pleura is extremely rare. The first case report in China was described. Methods The clinical data of a case of primary liposarcoma of the pleura diagnosed in this hospital were reported, and the pertinent literature was reviewed. Results A total of 17 cases of primary liposarcomas of the pleura, including the case reported herein, had been described in international literature. Primary pleural liposarcomas occur predominantly in males and older patients, and the myxoid histological subtype is common. The most common symptoms are chest pain and shortness of breath. Radiographic and surgical evaluation are important for its diagnosis. Surgical resection with adjuvant radiation therapy is recommended for the disease. Conclusion More data are required for the treatment and prognostic evaluation of the primary liposarcoma of the pleura.