布-加综合征135例临床回顾性分析

对2004年8月至2007年2月复旦大学附属中山医院收治的135例布-力口综合征患者进行回顾性分析。结果示135例患者中继发于恶性肿瘤105例（77．8％），无确切继发病因者29例（21．5％）；其临床表现以黄疸（69．6％）、腹水（48．2％）、腹胀（40．7％）、下肢水肿（37．O％）为多见；可出现胆红素升高、凝血酶原时间延长、血清γ-谷氨酰转移酶升高；非创伤性辅助检查中可选择彩色多普勒血管超声、CT和MRI，阳性率分别为59．5％、69．5％、81．5％；血管造影术是诊断布-力口综合征的金标准；治疗方法以经皮血管内支架植入和（或）球囊扩张术为主，辅以溶栓、抗凝、抗血小板聚集和保肝、支持等内科治疗。提示布-力口综合征是一种临床综合征，但由于发病原因复杂、临床表现多样、实验室检查缺乏特异性，临床诊断难度增加。而血管造影术和支架植入治疗是行之有效的诊治方法。

Retrospective Analysis of Budd-Chiari Syndrome in 135 Patients

A total of 135 patients diagnosed with Budd-Chiari syndrome(BCS)during August 2004 and February 2007 were reviewed and analyzed retrospectively.The results showed that 105 subiects (77.8%)caused by malignances,while 29 participants(21.5%)had no definite pathogens.The most commonly seen symptom included jaundiee(69.6%),followed by ascites(48.2%),abdominal distention (40.7%)and lower extremity edema(37.0%).Hisher levels of STB,PT and γ-GT were determined.Color Dopple ultrasound,CT and MRI could be helpful in diagnosing BCS;angiography remained the most accurate measurement.Main treatment strategies were stent implantation and/or balloon dilation.BCS is a clinical syndrome with no typical symptoms.which makes its management very difficult.A complete understanding of the condition will help reduce misdiagnosis.Angiography and stent implantation are primary ways to diagnose or treat BCS.