小儿乙状结肠冗长症病理特点分析

目的 探讨小儿乙状结肠冗长症的病理特点，以提高对该症病理特点的认识。方法 分析我科1993～2002年间经手术治疗12例小儿乙状结肠冗长症的临床病理资料。结果 小儿乙状结肠冗长症病理特点与先天性巨结肠同源病相似。主要表现为乙状结肠肠壁肥厚，部分肌纤维变性。结肠黏膜萎缩，黏膜下充血水肿；肌间神经丛减少，均可见神经节细胞发育幼稚，且数量减少或体积变小，呈固缩或空泡变性。结论 小儿乙状结肠冗长症大多有肠神经元发育异常。

Analysis on pathologic characters of Dolichasigmoid in children

Objective To explore pathologic characters and improve the recognition of the characters of Dolichasigmoid in children.Methods The pathological data of 12 cases of Dolichasigmoid subject to operation from 1993 to 2002 were analyzed.Results Pathologic characters of Dolichasigmoid in children,which were similar to allied disorders of Hirschsorung's disease(ADHD),mainly include:thickening of the wall of sigmoid;partial myofibrosis;atrophy of mucosa;hyperemia and edema of submucosa;deduction of myenteric nerve plexus;formation of megaganglion,immature of ganglion cell,which has not only quantity decrease or volume deduction,but also Pyknosis and Vacuole degeneration.Conclusion Dolichasigmoid in children mostly has neuronal intestinal malformations.