| 儿童心肌致密化不全的临床表现及预后 |
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| 引用本文： | 陈莉. 儿童心肌致密化不全的临床表现及预后[J]. 国际儿科学杂志, 2014, 41(2): 117-119,123 |
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| 作者姓名： | 陈莉 |
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| 作者单位： | 陈莉 (400014,重庆医科大学附属儿童医院心内科)； |
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| 摘 要： | 心肌致密化不全是一种与基因相关的遗传性心肌病,以心室内异常粗大的肌小梁和交错的深隐窝为特征.心肌致密化不全病因及发病机制不清.心肌致密化不全临床少见,预后较差.该文就儿童心肌致密化不全的临床表现及预后进行阐述,加深对儿童心肌致密化不全的认识,提高临床诊治水平,提高患者生存质量,延长患儿生存期.
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| 关 键 词： | 心肌致密化不全 临床表现 预后 儿童 |
Clinical and prognosis of the children with noncompaction of ventricular myocardium |
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| Affiliation: | Chen Li, Lyu Tiewei.( 1.Department of Cardiology, Children＇ s Hospital of Chongqing Medical University, Chongqing 400014,China;) |
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| Abstract: | Noncompaction of ventricular myocardium （NVM） is reported as a genetic disease characterized by excessively prominent trabeculations and deep intertrabecular recesses.The etiology and pathogenesis are unclear.NVM is a rare disease with poor prognosis.The purpose of this areide is to review NVM manifestations and prognosis,to enhance the awareness of NVM,to improve the diagnosis and treatment,to ensure a better life quality and to increase the lifetime of NVM patients. |
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| Keywords: | Noncompaction of ventricular myocardium Manifestation Prognosis Children |
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