Broncheoalveolar carcinoma associated with pulmonary lymphangioleiomyomatosis and Tuberous Sclerosis Complex: case report |
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| Authors: | Carneiro Cláudia Gupta Narainder |
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| Affiliation: | a Department of Radiology, Instituto Portugues de Oncologia Francisco Gentil, Porto. Portugal, Rua Dr. António Bernardino de Almeida 4200-072 Porto, Portugal;b Department of Radiology, Thomas Jefferson University Hospital, 1087 Main Bldg. 132 S. 10th Street Philadelphia, PA 19107-5244, USA |
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| Abstract: | Lymphangioleiomyomatosis (LAM) is a rare disorder that predominantly affects the lung parenchyma of young women and it's characterized by pulmonary cyst. Tuberous sclerosis complex (TSC) is a rare genetic disorder presenting with hamartomas and neurologic symptoms. The two renal pathologies most commonly seen in TSC are angiomyolipomas and cysts; less commonly, TSC co-exist with polycystic kidney disease. In this report is described an uncommon case of a patient with broncheoalveolar carcinoma, pulmonary LAM and TSC with polycystic kidney disease. |
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| Keywords: | Lymphangioleiomyomatosis Tuberous sclerosis complex Angiomyolipomas Polycystic kidney disease Broncheoalveolar carcinoma |
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