Metabolic storage diseases: amyloidosis |
| |
Authors: | Brunt Elizabeth M Tiniakos Dina G |
| |
Affiliation: | Department of Pathology, Saint Louis University School of Medicine, 4(th) Floor, SLUH, 3635 Vista Avenue, St. Louis, MO 63110, USA. bruntem@slu.edu |
| |
Abstract: | This article provides an overview of the current concepts in pathogenesis, epidemiology, clinical significance, and treatment options for amyloidosis. Emphasis is given to hepatic amyloidosis, which ranges from a clinically insignificant histologic curiosity to a harbinger of widespread disease accompanied by a poor prognosis. Clinical characteristics and clues to the diagnosis are discussed as well as the importance of histologic confirmation and the controversy surrounding liver biopsy. |
| |
Keywords: | |
本文献已被 PubMed 等数据库收录! |
|