婴幼儿原发性心脏肿瘤的诊断与治疗

目的:总结婴幼儿原发性心脏肿瘤的诊断和治疗经验。方法:回顾性分析2013年8月至2019年2月大连医科大学附属大连市儿童医院心脏中心收治的7例疑似原发性心脏肿瘤婴幼儿的诊治过程，患儿均行超声心动图等检查明确诊断，根据肿瘤的大小和位置选择治疗方案。出院后行随访观察。结果:7例患儿均经超声心动图诊断为原发性心脏肿瘤，其中2...

Diagnosis and treatment of primary cardiac tumors in pediatric patients

Objective To summarize the experience in diagnosis and treatment of primary cardiac tumors in pediatric patients.Methods Retrospectively analyzing 7 pediatric patients who were suspected as primary cardiac tumors and diagnosed and treated in Department of Heart Center,Children′s Hospital of Dalian Medical University from August 2013 to February 2019.All patients underwent echocardiography and other examinations,so as to confirm the diagnosis and the treatment plan was chosen based on the size and location of the tumor.All patients were followed up after discharge.Results A total of 7 patients were diagnosed as primary cardiac tumors by echocardiography,among which 5 cases underwent surgical treatment,and 2 cases were diagnosed with tuberous sclerosis without surgery.In children undergoing surgery,1 patient underwent autologous heart transplantation to remove the tumor,1 patient had arrhythmia,1 patient had mitral regurgitation after surgery,and the mitral regurgitation was corrected again.The remaining children had no adverse complications and were discharged successfully.Histologic examination revealed rhabdomyoma in 4 patients,and fibroma in 1 patient.The patients were followed up for 2-66 months after discharge,and no tumor recurrence was observed in the children who performed surgery.There was a trend of spontaneously regress of cardiac tumor in 2 patients without surgery.Conclusions Echocardiography is the first choice for the diagnosis of primary cardiac tumors in Pediatric patients.Rhabdomyoma is the most prevalent histologic type of primary cardiac tumors,and tuberous sclerosis should be excluded during the diagnosis process.Patients with tuberous sclerosis selected conservative treatment,and surgical treatment was selected for children with obvious symptoms.According to the location and size of lesion,therapy strategies should be chosen and autologous heart transplantation can be adopted to remove the tumor for children with large tumors.Autologous heart transplantation to remove the tumor is a good surgical treatment.