腹膜后腺泡状软组织肉瘤1例

腺泡状软组织肉瘤是一种少见的软组织恶性肿瘤,发生于腹膜后的腺泡状软组织肉瘤极为罕见,主要表现为无痛性生长的软组织肿块.国内外报道罕见,且易与副神经节瘤、腺泡状横纹肌肉瘤、肾透明细胞癌、颗粒细胞瘤混淆.本文报道腹膜后的腺泡状软组织肉瘤1例,结合影像学、临床病理学特征、免疫组织化学及基因检测技术,作出了正确诊断及治疗,并结合相关文献进行分析讨论,进一步提高了对腹膜后的腺泡状软组织肉瘤的认识.

Retroperitoneal alveolar soft-part sarcoma:A case report

Alveolar soft-part sarcoma is a rare type of malignant soft tissue tumor that usually presents as a painless,slow-growing mass and is easily misdiagnosed as paraganglioma,alveolar rhabdomyosarcoma,clear cell renal cell carcinoma,or granular cell tumor.Alveolar soft-part sarcoma of the retroperitoneum is extremely rare.Here we report a case of retroperitoneal alveolar soft–part sarcoma that was correctly diagnosed based on a combination of imaging,clinical and pathological features and the use of immunohistochemical and gene detection techniques.A literature review was performed to further raise the awareness of this rare disease.