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播散型匐行性穿通性弹性纤维病1例
引用本文:闫洁,叶庆佾,郝飞,杨希川.播散型匐行性穿通性弹性纤维病1例[J].临床皮肤科杂志,2006,35(3):160-161.
作者姓名:闫洁  叶庆佾  郝飞  杨希川
作者单位:第三军医大学西南医院皮肤科,重庆,400038
摘    要:报告1例播散型匐行性穿通性弹性纤维病。患者男,17岁。全身出现成片丘疹伴轻度瘙痒8个月。皮肤科检查示面颈部、躯干、四肢泛发对称的米粒大红色角化性丘疹,排列成线状、环状、半环状或匐行状。组织病理检查显示:表皮角化过度,棘层肥厚,部分表皮穿通,形成管道,真皮上部弹性纤维增多呈嗜碱性变性,其周围可见混合性炎性细胞及嗜碱性碎片组成的异物肉芽肿。

关 键 词:匐行性穿通性弹力纤维病  播散型
文章编号:1000-4963(2006)03-0160-02
收稿时间:2005-04-26
修稿时间:2005-04-262005-06-06

Disseminated elastosis perforans serpiginosa: a case report
YAN Jie,YE Qing-yi,HAO Fei,YANG Xi-chuan.Disseminated elastosis perforans serpiginosa: a case report[J].Journal of Clinical Dermatology,2006,35(3):160-161.
Authors:YAN Jie  YE Qing-yi  HAO Fei  YANG Xi-chuan
Institution:Department of Dermatology, Southwest Hospital, the Third Military Medical University, Chongqing 400038, China
Abstract:A 17-year-old man with disseminated elastosis perforans serpiginosa is reported. The patient had grouping papules on the skin with light pruritus for 8 months. The clinical manifestations included disseminated, symmetrical and keratotic papules which were grouped in linear, arciform, circular, or serpiginous patterns on the face, neck, trunk and extremities. The histopathologic findings showed that basophilic degenerated elastic fibers were extruded from superficial corium. The degenerated elastic fibers were surrounded with the imflammatory ceils and basophilic cell debris, which formed a foreignbody granuloma.
Keywords:elastosis perforans serpiginosa  disseminated
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