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Hallervorden-Spatz综合征的MRI诊断
引用本文:袁建军,程文君,康五根,仲海. Hallervorden-Spatz综合征的MRI诊断[J]. 医学影像学杂志, 2014, 0(6): 902-905
作者姓名:袁建军  程文君  康五根  仲海
作者单位:[1]浙江省台州市立医院放射科,浙江台州318000 [2]山东大学第二医院影像科,山东济南250033
摘    要:目的:探讨Hallervorden-Spatz综合征的颅脑M RI诊断价值,提高对该病的认识。方法回顾性分析2007年2月~2012年4月经临床证实为 Hallervorden-Spatz综合征的4例患者颅脑MRI资料。结果 Hallervorden-Spatz综合征颅脑M RI表现为:双侧苍白球、黑质T2 WI像对称性低信号,苍白球低信号的前内侧出现斑点状高信号,即典型的“虎眼征”。SWI像上病灶呈低信号,MRS检查可见NAA、NAA/Cr及Cho/Cr下降。结论 Hallervorden-Spatz综合征具有典型的MRI表现,MRI检查在Hallervorden-Spatz综合征中有重要的诊断价值。

关 键 词:Hallervorden-Spatz综合征  磁共振成像  诊断

MRI diagnosis of Hallervorden-Spatz syndrome
YUAN Jian-jun,CHENG Wen-jun,KANG Wu-gen,ZHONG Hai. MRI diagnosis of Hallervorden-Spatz syndrome[J]. Journal of Medical Imaging, 2014, 0(6): 902-905
Authors:YUAN Jian-jun  CHENG Wen-jun  KANG Wu-gen  ZHONG Hai
Affiliation:1. Department of Radiology, Taizhou City Hospital, Zhejiang Province, 318000, P. R. China; 2. Department of Radiology, The Second Hospital of Shandong Universtiy , Shandong , Jinan 250033, P. R. China)
Abstract:Objective To investigate the diagnostic value of MRI in Hallervorden-Spatz syndrome .Methods MRI data of Hallervorden-Spatz syndrome in 4 patients in our hospital from February 2007 to April 2012 were retrospectively analyzed .Results The brain MRI of Hallervorden-Spatz syndrome was demonstrated abnormalities confined to the pallidum , which presented diffuse low signal intensity in SWI ,and eye-of-the-tiger sign in T2 WI .Compared with the normal brain tissue ,the NAA ,NAA/Cr ,Cho/Cr were decreased .Conclusion Hallervorden-Spatz syndrome has definite MR imaging findings ,and M RI is of important value in diagnosis of Hallervorden-Spatz syndrome .
Keywords:Hallervorden-Spatz syndrome  Magnetic resonance imaging  Diagnosis
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