Recurrent pancreatitis in Caroli's disease. Treatment by endoscopic sphincterotomy

'Pure' Caroli's disease is rarely observed, usually presenting with symptoms of cholangitis: cases of pancreatitis seem most infrequent in the literature. A case of recurrent pancreatitis in Caroli's disease associated with renal policystic disease is presented: the rareness of this manifestation is stressed and the possible pathogenetic hypotheses are discussed, as well as indications for the selected treatment by endoscopic sphincterotomy.