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成人法洛三联症彩色多普勒超声心动图特征和规律性研究
引用本文:侯传举,胡斌,邓东安,朱鲜阳,韩秀敏,张端珍,王琦光.成人法洛三联症彩色多普勒超声心动图特征和规律性研究[J].医学影像学杂志,2011,21(11):1657-1661.
作者姓名:侯传举  胡斌  邓东安  朱鲜阳  韩秀敏  张端珍  王琦光
作者单位:1. 沈阳军区总医院先心病内科辽宁 沈阳 110840
2. 武警辽宁总队医院院办辽宁沈阳 110034
摘    要:目的:探讨成人法洛三联症(TOF)彩色多普勒超声心动图(CDE)特征和规律性,分析房间隔缺损(ASD)血流动力学与肺动脉瓣狭窄(PS)程度的关系,提高诊断准确率。方法:应用CDE检查62例成人TOF(14~57岁,平均24.8岁),二维超声心动图(2DE)测量ASD大小,连续多普勒(CW)估测跨肺动脉瓣压力阶差,与心导管和手术对照。其中52例行心导管检查,14例行介入治疗,48例外科手术治疗。结果:根据CDE特征表现对56例做出正确诊断,诊断准确率90.3%,误诊继发孔ASD和PS各3例。2DE测量ASD直径5~33(18±12)mm与手术测量ASD直径7~35(21±13)mm呈正相关(r=0.52,P〈0.001);CW估测跨肺动脉瓣压力阶差36~154(93±52)mmHg与心导管测量跨肺动脉瓣压力阶差30~140(86±50)mmHg呈正相关(r=0.67,P〈0.001)。彩色多普勒血流显像(CDFI)显示过房间隔分流束血流信号,其中左向右(61.3%)、双向(22.6%)、右向左(11.3%)和无分流(4.8%)。根据CDE筛选14例适应证实施介入治疗全部获得成功。结论:成人TOF的CDE特征明显,CDFI显示过ASD分流束血流信号呈多样化,与PS程度密切相关,CDE对成人TOF有特异性诊断价值,介入治疗前应用CDE判断ASD大小、位置和PS程度非常重要。

关 键 词:先天性心脏病  法洛三联症  彩色多普勒超声心动图

Study on characteristics and regularity of color Doppler echocardiography in adult trilogy of fallot
HOU Chuan-ju,HU Bin,DENG Dong-an,ZHU Xian-yang,HAN Xiu-min,ZHAGN Duan-zhen,WANG Qi-guang.Study on characteristics and regularity of color Doppler echocardiography in adult trilogy of fallot[J].Journal of Medical Imaging,2011,21(11):1657-1661.
Authors:HOU Chuan-ju  HU Bin  DENG Dong-an  ZHU Xian-yang  HAN Xiu-min  ZHAGN Duan-zhen  WANG Qi-guang
Institution:HOU Chuan-ju1,HU Bin2,DENG Dong-an1,ZHU Xian-yang1,HAN Xiu-min1,ZHAGN Duan-zhen1,WANG Qi-guang1 1.Department of Congenital Heart Disease Internal,Shenyang Military General Hospital,Shenyang 110840,P.R.China 2.Admhistratve Offile Liaoning Provincial Lorps Hospital,Shenyang 110034,P.R.China
Abstract:Objective:To study the imaging characteristics and regularity of color Doppler echocardiography(CDE) of adult trilogy of Fallot(TOF),to analyze the relationship between the hemodynamics of atrial septal defect(ASD) and the degree of pulmonary stenosis(PS) and to improve the diagnostic accuracy.Methods:Sixty-two patients with adult TOF(14~57 years old,mean 24.8 years old) were examined by CDE,ASD size were measured by two-dimensional echocardiography(2DE),and transpulmonary valve pressure gradient was estima...
Keywords:Congenital heart disease  Trilogy of Fallot  Color Doppler echocardiography  
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