Surgical treatment of macrodactyly in Proteus syndrome

Proteus syndrome is a rare congenital disorder composed of a wide variety of deformities including macrodactyly of the foot. A dearth of information on the surgical management of macrodatyly in Proteus syndrome exists in the literature. In this report, we present our experience in the surgical treatment of two patients with Proteus syndrome, both of whom suffered from disordered gait and problems with finding well-fitting shoes. By resection of the most enlarged ray, shortening of adjacent enlarged rays, debulking of soft tissue and ray transposition, both patients gained a fairly normal gait and were able to wear normal shoes.