视盘毛细血管瘤的临床表现及荧光素眼底血管造影特征

目的 观察视盘毛细血管瘤的临床表现及其荧光素眼底血管造影(FFA)的特征.方法 回顾性系列病例研究.分析9例(10眼)视盘毛细血管瘤的临床资料,包括眼底彩照及FFA.平均年龄(26.8±9.7)岁,4例(4眼)合并周边部视网膜毛细血管瘤,6例符合Von Hippel-Lindau病的临床诊断.结果 内生型8例(8眼),外生型1例(2眼).5眼瘤体位于视盘颢上、颢下或颢侧,3眼瘤体位于视盘中央并覆盖视盘表面.8例(9眼)行FFA检查者的FFA图像中,5眼呈现"冲刷"现象.结论 视盘毛细血管瘤多位于视盘颞侧或中央,瘤体周围伴有明显的视网膜水肿、渗出.内生型是常见的临床类型.FFA是重要的诊断和罄别诊断方法.

Clinical features and charactristics of fundus fluorescein angiography of juxtapapillary capillary hemangioma

Objective To describe the clinical features and characteristics of fundus fluorescein angiography (FFA) of juxtapapillary capillary hemangioma. Methods Retrospective case series study. Clinical data including fundus color photography from 10 eyes of 9 cases and FFA of 8 cases (9 eyes) were analyzed. The average age of the 9 cases was (26.8±9.7)years, and 4 eyes of 4 cases presented with peripheral retinal capillary hemangiomas. Six cases with 7 affected eyes were diagnosed with Von Hippel-Lindau disease. Results The type of tumor growth was endophytic in 8 eyes of 8 cases, and exophytic in both eyes of one case. The location of the growth relative to the disc was temporal, inferotemporal, or superotemporal in 5 eyes, and central on the disc in 3 eyes. In 9 eyes of 8 cases underwent FFA, FFA graph revealed "wash out" in the late phase in 5 eyes. Conclusion Juxtapapillary capillary hemangiomas often locate on the temporal or center of the disc. Associated lesions include retinal exudation and edema around the tumor. The type of tumor growth was more commonly endophytic. FFA is a vital ancillary test in distinguishing juxtapapillary hemangiomas from other diseases.