Double-outlet left ventricle

Origin of both great vessels from the left ventricle is an uncommon congenital cardiac anomaly. When there is an associated ventricular septal defect and pulmonary stenosis, the preoperative diagnosis has usually been that of tetralogy of Fallot. Operative repair was accomplished successfully in a 12-year-old boy with such a combination of defects. This involved patch closure of the ventricular septal defect, interruption of blood flow from the left ventricle to the pulmonary artery by suture closure of the pulmonary valve and annulus, and restoration of blood flow to the lung by using a Dacron tube conduit between the right ventricle and the distal main pulmonary artery. This represents the third successful operative repair of double-outlet left ventricle.