Sturge—Weber综合征

Sturge—Weber综合征是一种以面部毛细血管畸形、软脑膜血管瘤和眼血管畸形为特征的神经皮肤综合征。鲜红斑痣皮损累及整个三又神经眼支或双侧分布提示合并潜在的神经系统及眼的损害。增强核磁共振成像是诊断Sturge—Weber综合征最敏感的方法。治疗上，鲜红斑痣采用脉冲染料激光治疗，癫痫和青光眼采用药物或手术控制。

Sturge-Weber syndrome

Sturge-Weber syndrome is a sporadic neurocutaneous syndrome characterized by facial capillary malformation, ocular vascular malformation and leptomeningeal angioma. The involvement of whole ophthalmic branch of trigeminal nerve and bilateral face by port-wine stains often strongly predicts the presence of underlying neurological and/or ocular disorders that require on-going ophthalmological surveillance and/or neurological management. Magnetic resonance imaging （MRI）, especially after contrast injection, is the preferred and most sensitive imaging technique for the diagnosis of Smrge-Weber syndrome. Facial port wine stain can be treated with pulsed dye laser, and the control of epilepsy and glaucoma may be achieved by medical treatment and surgical operation.