ILL型右室双出口(附一例报告)

<正> 全内脏转位合并镜面右位心是心脏原发位置异常,多无其他心脏畸形,但在先天性心脏畸形中有全内脏转位的发生率可达0.8%。最常见的合并畸形是纠正型大动脉转位。右室双出口是大动脉转位的一种,即主动脉及肺动脉均发自右心室,较为少见。全内脏转位、镜面右位心合并右心室双出口更为少见,本院曾收治一例,介绍如下: 临床资料王×(住院号21821)女、13岁,自幼发现心脏杂音,经检查为室间隔缺损、肺动脉高压,合并内脏转位、右位心,转来本院。患儿生后易患感冒、肺炎。近两年来有劳累后心

ILL-DORV—A CASE REPORT

Situs Inversus, mirror image dextroposition of the heart with double outlet right ventricle is of rare occurence. There are difficulties in the clinical diagnosis especially those with no or mild cynosis (subcristal ventricular septal defect without pulmonary stenosis and low pulmonary vascular resistance) which presents with a picture similar to simple ventricular septal defect with pulmonary hypertension. We found that cases of ventricular septal defect with pulmonary hypertension and mild right to left shunt who showed prominent systolic murmur,increased pulmonary blood flow and left ventricular hypertrophy, left axis deviation on EKG should do angiocardiography to rule out DORV which can be corrected surgically.