Caroli病的CT诊断(附7例分析)

目的　探讨Caroli病的CT表现及诊断价值。方法　回顾性分析 7例Caroli病的临床和CT资料。结果　Caroli病Ⅰ型 1例 ,CT表现为肝右叶近肝门区肝内胆管呈囊状扩张 ,伴肝内胆管多发结石 ,无肝硬化、脾肿大和门脉高压。Caroli病Ⅱ型 6例 ,CT均表现为肝内多发低密度影 ,增强扫描后无强化 ,可以清晰显示扩张的肝内胆管 ,呈囊状或柱状扩张 ,并沿胆管走行分布 ;均合并有肝硬化、脾肿大及门静脉侧支循环开放 ,合并胆管结石 5例、肝脓肿 1例、腹水 1例。结论　CT对Caroli病的诊断及明确病变范围有重要价值。

CT Diagnosis of Caroli Disease (Analysis of 7 Cases)

Purpose To study the CT manifestation and diagnostic value in Caroli disease. Methods Clinical and CT findings in 7 cases of Caroli disease were retrospectively analyzed. Results One was simple type which CT findings of the liver showed saccular dilatation of the right lobe intrahepatic bile ducts and multiple intraductal calculus,there was no evidence of cirrhosis,splenomegaly,or other findings of portal hypertension.Six were periportal fibrosis type which transverse CT imaging of the liver showed multiple rounded or cylindrical hypodensity structures which were consistent with the distribution of intrahepatic bile ducts by plain scanned and no enhancement on contrast material enhanced CT examination,and there were cirrhosis,hepatosplenomegaly and the opening of portal vein collateral pathway in all six patients,accompanying with intraductal calculus ( n =5),acute hepatic abscesses ( n =1),and ascites ( n =1). Conclusion CT is a valuable method to establish the diagnosis and demonstrate the extent of Caroli disease.