原发性肺动脉高压症(附7例报告)

对7例原发性肺动脉高压的临床及 X 线所见进行了分析。本病由原因不明的肺内细小动脉阻塞形成,较为罕见,多发生在青年女性。临床表现不具特征性。胸片显示右室肥大,肺动脉段膨隆,右下肺动脉增粗(平均宽度21.6mm)。然而,远侧肺动脉纤细,肺野清晰,透光度增加。诊断本病须排除继发性肺动脉高压,有时需进行心导管检查以除外轻微隐匿的先心病。

PRIMARY PULMONARY HYPERTENSION(A REPORT OF SEVEN CASES)

The clinical and X-ray findings in seven cases with primary pulmonary hype rtension were analysed.Primary pulmonary hypertension is a rare condition.There is obstruction of unknown cause in the terminal arteries and arterioles of the lungs.The disease mostly occured in young women.Symptoms include dyspnea on exertion,muscular weakness and syncope on effort.The ECG shows signs of right ventricular strain or hypertrophy.Chest Roentgenogram shows right ventricle hypertrophy.The pulmonary artery segment is prominent.The right descending branch of the pulmonary artery is widened (average 21.6mm in width).However,the branches of the distal pulmonary arteries are small and the peripheral lung field is clear.The diagnosis depends on eliminating the known secondary forms of pulmonary hypertention.Sometimes cardiac catherterization is necessary to exclude remote possibilities of occult congenital heart disease.