A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach |
| |
| Institution: | 1. Division of Reproductive Immuno-Endocrinology, Department of Obstetrics and Gynecology, Faculty of Medicine Universitas Indonesia, Dr. Cipto Mangunkusumo Hospital Jakarta, Indonesia;2. Department of Obstetrics and Gynecology, Dr. Cipto Mangunkusumo Hospital Jakarta, Faculty of Medicine Universitas Indonesia, Pangeran Diponegoro Street No. 71, Kenari, Jakarta, Indonesia;3. Indonesian Reproductive Medicine Research and Training Center (INA- REPROMED), Faculty of Medicine Universitas Indonesia, Dr. Cipto Mangunkusumo Hospital Jakarta, Pangeran Diponegoro Street No. 71, Kenari, Central of Jakarta, 10430, Indonesia |
| |
| Abstract: | Mayer Rokitansky Kuster Hauser (MRKH) syndrome is a congenital disorder involving reproductive, genitourinary, bone, and cardiac malformation. The incidence is 1 in 4000–5000 females livebirths. The phenotype is female 46 XX karyotype, normal secondary sexual characteristics, and normal functional ovaries. The occurrence of leiomyoma in uterine remnant in MRKH syndrome is a very rare case, even though several cases have been reported. The diagnosis and management approach, in this case, is quite challenging. Here, we report a 38 years old female who represents multiple leiomyomas on the rudimentary uterus, then we did laparoscopic removal of the fibroids and adjacent rudimentary uterus. |
| |
| Keywords: | Mayer Rokitansky Kuster Hauser (MRKH) syndrome Multiple leiomyomas Rudimentary uterus Laparascopic Case report |
| 本文献已被 ScienceDirect 等数据库收录！ |
|
