Down综合征并发先天性心脏病的临床分析 |
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引用本文: | 王琦光,朱鲜阳,韩秀敏,张端珍,崔春生,陈火元,肖家旺.Down综合征并发先天性心脏病的临床分析[J].心功能杂志,2014(1):43-45,55. |
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作者姓名: | 王琦光 朱鲜阳 韩秀敏 张端珍 崔春生 陈火元 肖家旺 |
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作者单位: | 沈阳军区总医院先心病内科,辽宁沈阳110016 |
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摘 要: | 目的:总结分析Down综合征(Down’s syndrome)并发的先天性心脏病畸形及血流动力学资料。方法:2008年7月-2012年10月,采用经胸二维超声心动图并彩色多普勒显像及右心导管/心血管造影检查方法,诊断36例并发先心病的Down综合征患者,本文通过36例临床资料分析,探讨Down综合征并发的先心病畸形及其血流动力学。结果:36例患者中室间隔缺损(VSD)10例,房室间隔缺损(AVSD)6例,动脉导管未闭(PDA)6例,房间隔缺损(ASD)2例,ASD+PDA2例,ASD+VSD1例,ASD+PDA+VSD1例,VSD+PDA4例,PDA十二叶主动脉瓣(BAV)1例,法洛四联症(TOF)2例,TOF+ASD1例,18例有肺动脉高压者,其中5例为阻力型肺动脉高压。结论:①Down综合征并发的心血管畸形中,以VSD、AVSD和PDA最为常见,并常并发ASD、TOF。②在无肺动脉狭窄的患者中,约50%并发有肺动脉高压。
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关 键 词: | Down综合征 先天性心脏病 心脏畸形 心导管检查 肺动脉高压 |
Clinical analysis of Down syndrome with congenital heart diseases |
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Authors: | WANG Qi-guang ZHU Xian-yang HAN Xiu-min ZHANG Duan-zhen CUI Chun-sheng CHEN Huo- yuan XIAO Jia-wang |
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Institution: | (Department of Congenital Heart Disease, General Hospital, Shenyang Military Area Command, Shenyang 110016, Liaoning, China) |
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Abstract: | AIM: To analyze congenital heart deformity and hemodynamic data of Down syndrome. METHODS : Clinical data of Down' s syndrome with congenital heart disease and its hemodynamics were analyzed in 36 patients diagnosed with congenital heart disease patients with Down syndrome by transtho- racic two-dimensional echoeardiography, color Doppler flow imaging and right heart catheterization or angiocardiography from July 2008 to October 2012. RESULTS: Among the 36 cases, there were ten patients with VSD, six patients with AVSD, six patients with PDA, two patients with ASD, two cases with ASD + PDA, one case with ASD + VSD, one patient with ASD + PDA + VSD, four patients with VSD + PDA, one patient with PDA + BAV, two patients with TOF 2, and once patient with TOF + ASD. Eighteen patients had pulmonary hypertension including five cases of resistant pulmonary arterial hyper- tension. CONCLUSION: In cardiovascular malformations with Down syndrome, VSD (28%), AVSD ( 17% ) and PDA ( 17% ) are most common and are often associated with ASD or TOF. In patients with- out pulmonary artery stenosis, about half are complicated with pulmonary artery hypertension. |
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Keywords: | Down syndrome congenital heart disease cardiac abnormalities cardiac catheterization pulmonary arterial hypertension |
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