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晚发性脊椎骨骺发育不良伴进行性关节病
引用本文:郭琪!710068,陈志刚,杨广夫,马茂林,钱致中. 晚发性脊椎骨骺发育不良伴进行性关节病[J]. 实用放射学杂志, 1996, 0(6)
作者姓名:郭琪!710068  陈志刚  杨广夫  马茂林  钱致中
作者单位:陕西省人民医院放射科(郭琪!710068),西安医科大学第一附属医院影像中心(陈志刚,杨广夫,马茂林,钱致中)
摘    要:本文报告3例晚发性脊椎骨骺发育不良伴进行性关节病.临床儿童期出现进行性关节肿痛挛缩,成人后关节肥大畸形,可出现脊髓受压表现.X线特点为椎体普遍变扁,关节肥大退变,骨骺变形碎裂,骨盆发育异常.MR表现椎间盘变性膨出,脊髓受压.

关 键 词:骨发育异常  关节病

Spondyloepiphyseal Dysplasia Tarda with Progressive Arthropathy
Guo Qi Chen Zhigang Yang Guangfu et al.. Spondyloepiphyseal Dysplasia Tarda with Progressive Arthropathy[J]. Journal of Practical Radiology, 1996, 0(6)
Authors:Guo Qi Chen Zhigang Yang Guangfu et al.
Affiliation:Guo Qi Chen Zhigang Yang Guangfu et al.
Abstract:Three cases of SEDTPA were reported. The disease presents clinically in mid-childhood as progressive contracture. It presents in adult as features of compression of spinal cord. The X-ray features are generalized platyspondyly, degenerative arthropathy, deformative and brocken epiphyses, and pelvis abnormality. The MR features are degeneration and protrusion of intervertebral disc, and compresson of sinal cord.
Keywords:Osteodysplasia Arthropathy  
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