儿童组织细胞增生症X颅骨病变的影象学诊断

分析儿童组织细胞增生症X颅骨病变的影像学表现和特点，并结合病理阐述其在临床诊断中的价值。材料和方法：回顾性分析经病理证实的儿童组织细胞增生症X伴颅骨破坏者21例，其中男性16例，女性5例。年龄从8个月～9岁，平均3．8岁。除X线平片外，13例还进行了CT扫描，其中单纯平扫5例，平扫＋增强8例。结果：21例颅骨破坏中，颅顶部破坏20例，占95％；颅底部9例，占42．9％；眼眶7例，占33．3％；面颅骨3例，占143％。结论：本症颅骨病变在X线影像学上有较特殊的表现，是临床诊断和鉴别诊断的重要手段，有时甚至可起到决定性的作用，并能有助于观察疗效，了解有无复发等。

Imaging Diagnosis of the Skull Lesions in Children Histiocytosis X

To analyse the imaging features of the skull lesions in children with histiocytosis X, combining the pathology to explain its importance in clinical diagnosis. Materials and Methods: 21 cases of children histiocytosis X with skull lesions proven by pathology included 16 males and 5 females, aging from 8months to 9 years with average of 3. 8 years old. All Patients had X-ray plain films. 13 were further examined by CT with 8 of enhancement. Results: Among 21 cases with skull lesions, calvarium distructions being in 20 cases, about 95%; distruction of the base of skull in 9 case, 42. 9%; orbital bones 7cases, 33. 3%; facial bones 3 cases, 14. 3%. Conclusion: The characteristic features of X-ray imaging in skull lesions of the disease take a great part in clinical diagnosis and differential diagnosis, furthermore also important for the follow up and early detection of recurrence.