Diffuse splenic and visceral hemangiomas complicated by chronic consumption coagulopathy |
| |
| Authors: | Helen Platokouki Sophie Aronis Angeliki Mitsika Demetrios Keramidas Efstathios Harokopos |
| |
| Institution: | Hemostasis Unit, Athens University, Aghia Sophia Children's Hospital, Athens, Greece;Second Department of Surgery, Athens University, Aghia Sophia Children's Hospital, Athens, Greece;First Department of Paediatrics, Athens University, Aghia Sophia Children's Hospital, Athens, Greece |
| |
| Abstract: | Abstract The case of a 7-year-old girl with a 2 year history of easy bruising associated with thrombocytopenia is reported. On admission she presented with ecchymoses, abdominal distention and splenomegaly. Hemostasis investigation revealed a consumption coagulopathy. Several radiological studies failed to confirm the diagnosis of diffuse splenic and visceral hemangiomatosis, which was eventually estasblished by an explorative laparotomy. Platelet count and the other coagulation abnormalities progressively returned to normal after splenectomy, although the remaining hemangiomas were extensive. |
| |
| Keywords: | consumption coagulopathy Kasabach Merritt Syndrome spleen hemangioma visceral hemangiomatosis |
|
|
