Anaesthetic management of children with Joubert syndrome |
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| Authors: | WALID HABRE,CRAIG SIMS,MICHAEL D&#x SOUZA |
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| Affiliation: | WALID HABRE,CRAIG SIMS,MICHAEL D’SOUZA |
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| Abstract: | We report the anaesthetic management of two children with Joubert syndrome. Children with this syndrome have abnormalities of respiratory control due to changes in the brainstem and cerebellum. They are extremely sensitive to the respiratory depressant effects of anaesthetic agents, including nitrous oxide. Anaesthesia using inhalational induction, controlled ventilation, avoidance of opioids, and close postoperative monitoring is recommended. |
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| Keywords: | anaesthesia neurological disorders complications apnoea Joubert syndrome |
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