Protracted superficial Wegener granulomatosis in a child |
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Authors: | Ben Ghorbel Imed Dhrif Asma Sioud Miled Mohamed Houman Mohamed Habib |
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Affiliation: | Department of Internal Medicine, La Rabta hospital, Tunis, Tunisia. |
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Abstract: | Wegener granulomatosis is a rare, chronic, multisystemic vasculitis affecting mainly the upper and lower respiratory tracts together with glomerulonephritis, but the disease may involve any other organ. Protracted superficial form is a rare variant of the disease. We report a case of protracted superficial Wegener granulomatosis in a 16-year-old boy in whom the disease started with recurrent digital ulcers at age 7 years. Later, he developed nodules and papules associated with upper airway involvement and ocular keratitis without lung or renal involvement. C-ANCA was positive. The patient was treated with oral prednisone. Similar cutaneous and mucosal lesions developed during two relapses of the disease without renal or respiratory involvement. |
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