Ebstein's Anomaly with Subpulmonary Obstruction– A Rare Association |
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Authors: | Bhupinder Singh M.D. Anand Subramanyan M.D. D.M. M. Jayaranganath M.D. D.M. C. N. Manjunath M.D. D.M. |
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Affiliation: | Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, , Bangalore, Karnataka, India |
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Abstract: | Ebstein's anomaly comprises a wide spectrum of congenital cardiac abnormalities involving the tricuspid valve (TV) apparatus and the architecture of the morphological right ventricle (RV). We report a case of Ebstein's anomaly in a 3‐year‐old boy having a unique association with severe subpulmonic obstruction caused by tethered and dysplastic anterior tricuspid leaflet (ATL), and a large ventricular septal defect. In view of poorly functioning RV, the baby was planned for a bidirectional Glenn shunt with subsequent Fontan completion. |
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Keywords: | Ebstein's anomaly pulmonary valve ventricular septal defect |
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