Neonatal purpura fulminans due to homozygous protein C deficiency |
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Authors: | Ezer U Misirlioglu E D Colba V Ogoz E Kurt C |
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Abstract: | Severe and recurrent purpura fulminans developed in a Turkish boy at 1 week of age. Initial coagulation studies performed were compatible with disseminated intravascular coagulation. Subsequent investigations showed that the patient had homozygous and his healthy parents had heterozygous protein C deficiency. The episodes of purpura fulminans were controlled by infusions of fresh frozen plasma and heparinization. Oral anticoagulant therapy was given in the symptom-free period. |
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Keywords: | Homozygous Protein C Deficiency Newborn Purpura Fulminans |
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