| A Case of Erdheim—Chester Disease with Bilateral Orbital Involvement |
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| 引用本文： | WuZY YanJH 等. A Case of Erdheim—Chester Disease with Bilateral Orbital Involvement[J]. 眼科学报, 2001, 17(3): 163-167 |
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| 作者姓名： | WuZY YanJH 等 |
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| 作者单位： | [1]ZhongshanOphthalmicCenter,SunYat－senUniversityofMedicalSciences,Guangzhou,510060China [2]ZhongshanOphtha,SunYat－senUniversityofMedicalSciences,Guangzhou,510060China |
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| 摘 要： | Purpose: To describe a case of Erdheim-Chester disease with bilateral orbital involvement.Methods: A 43-year-old female with bilateral proptosis was presented. Its clinical features, image findings, pathological character and therapeutic effect were evaluated. Results: CT demonstrated bilateral, diffuse orbital mass. Histopathologic assessment revealed a diffuse xanthogranulomatous process with clusters of lipidladen histocytes. Numerous Touton giant cells were scattered throughout the lesion.Renal and heart failure happened during a 6-year follow-up period. Long bones roentgenogram demonstrated diffuse symmetrical sclerosis with extensive, lytic lesions. Systemic administration of corticosteroids, chemotherapy, immunoglobulin and traditional Chinese medicine showed good therapeutic result.Conclusions: An administration of systemic corticosteroids, chemotherapy, immuno-globin and traditional Chinese medicine can control Erdheim-Chester disease. Further exploration of its pathogenesis
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| 关 键 词： | Erheim－Chester病 眼眶浸润 治疗 |
A Case of Erdheim-Chester Disease with Bilateral Orbital Involvement |
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| Zhongyao Wu,Jianhua Yan,Wende Hong,Yaoxian Yuan,Lijun Dai. A Case of Erdheim-Chester Disease with Bilateral Orbital Involvement[J]. Eye science, 2001, 17(3): 163-167 |
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| Authors: | Zhongyao Wu Jianhua Yan Wende Hong Yaoxian Yuan Lijun Dai |
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| Affiliation: | 1. Zhongshan Ophthalmic Center, Sun Yat-sen University of Medical Sciences, Guangzhou, 510060 China
2. Department of Hemotology, The First Affiliated Clinical College Sun Yat-sen University of Medical Sciences, Guangzhou 510080 , China |
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| Abstract: | Purpose:To describe a case of Erdheim-Chester disease with bilateral orbital involvement.Methods:A 43-year-old female with bilateral proptosis was presented.Its clinical features,Image findings,pathological character and therapeutic effect were evaluated.Results:CT demonstrated bilateral,Diffuse orbital mass,Histopathologic assessment revealed a diffuse xanthogranulomatous process with clusters of lipidladen histocytes Numerous Touton giant cells were scattered throughout the lesion.Renal and heart failure happened during a 6-year follow-up period.Long bones roentgenogram demonstrated diffuse symmetrical sclerosis with extensive,lytic lesions Systemic administration of corticosteroids,Chemotherapy,immunoglobulin and traditional Chinese medicine showed good therapeutic result.Conclusions:An administraton of systemic corticosteroids,chemotherapy,immunoglobin and traditional Chinese medicine can control Erdheim-Chester disease.Further Exploration of its pathogenesis and collection of useful clincal data are required Eye Science 2001;17:163-167. |
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| Keywords: | Erdheim-Chester disease Orbit Treatment. |
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