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Natural history of Wolcott-Rallison syndrome: A systematic review and follow-up study
Authors:Denise Aldrian  Clemens Bochdansky  Anna M Kavallar  Christoph Mayerhofer  Asma Deeb  Abdelhadi Habeb  Andrea Romera Rabasa  Anuradha Khadilkar  Ahmet Uçar  Birgit Knoppke  Dimitrios Zafeiriou  Mariarosaria Lang-Muritano  Mohamad Miqdady  Sylvia Judmaier  Valerié McLin  Viktoriya Furdela  Thomas Müller  Georg F Vogel
Institution:1. Department of Paediatrics I, Medical University of Innsbruck, Innsbruck, Austria;2. Department of Paediatrics I, Medical University of Innsbruck, Innsbruck, Austria

Denise Aldrian and Clemens Bochdansky contributed equally to this study.;3. Paediatric Endocrinology Division, Sheikh Shakhbout Medical City, Khalifa University, Abu Dhabi, United Arab Emirates;4. Department of Pediatrics, Prince Mohamed bin Abdulaziz Hospital, National Guard Health Affairs, Madinah, Saudi Arabia;5. Department of Pediatric Anesthesia, Gregorio Marañón University Hospital, Madrid, Spain;6. Hirabai Cowasji Jehangir Medical Research Institute, Jehangir Hospital, Pune, India;7. Department of Pediatric Endocrinology & Diabetes, University of Health Sciences, Şişli Hamidiye Etfal Health Practices & Research Centre, Istanbul, Turkey;8. University Children's Hospital Regensburg (KUNO), University Medical Center Regensburg, Regensburg, Germany;9. 1st Department of Pediatrics, Hippokratio General Hospital, Aristotle University, Thessaloniki, Greece;10. Department of Endocrinology and Diabetology and Children's Research Centre, University Children's Hospital, Zurich, Switzerland;11. Division of Pediatric Gastroenterology, Sheikh Khalifa Medical City, Abu Dhabi, United Arab Emirates;12. Department of Paediatrics, LKH Hochsteiermark/Standort Leoben, Leoben, Austria;13. Department of Pediatrics, Gynecology and Obstetrics, Swiss Pediatric Liver Center, University of Geneva, Geneva, Switzerland;14. Department of Pediatrics, I. Horbachevsky Ternopil National Medical University, Ternopil, Ukraine

Abstract:
Keywords:acute liver failure  ER stress  neonatal-onset diabetes  paediatric  skeletal dysplasia
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